000 02222cam a22002417i 4500
020 _a9789400778924 (cloth)
020 _a9400778929 (cloth)
050 0 0 _aMED RC924
_b.P76
050 1 4 _aR850
_b.A392 v.802
245 0 0 _aProgress in heritable soft connective tissue diseases /
300 _aviii, 245 pages :
_billustrations (some color) ;
490 1 _aAdvances in Experimental Medicine and Biology,
505 0 _aStructure, physiology, and biochemistry of collagens -- Basic components of connective tissues and extracellular matrix: elastin, fibrillin, fibulins, fibrinogen, fibronectin, laminin, tenascins and thrombospondins -- Proteoglycans and diseases of soft tissues -- Advances in the use of growth factors for treatment of disorders of soft tissues -- Clinical, diagnostic, and therapeutic aspects of the Marfan syndrome -- Loeys-Dietz syndrome -- Connective tissue disorders and cardiovascular complications: the indomitable role of transforming growth factor-beta signaling -- The Ehlers-Danlos syndrome -- Ehlers-Danlos syndrome associated with glycosaminoglycan abnormalities -- Cutis laxa -- Collagen type VI myopathies -- Mouse models in tendon and ligament research -- Connective tissue disorders in domestic animals.
520 _a"This volume is a reference handbook focusing on diseases like Marfan syndrome, Ehlers-Danlos syndrome, Loeys-Dietz syndrome and other heritable soft connective tissue diseases. The book presents detailed information for both basic scientists and for clinicians seeing patients. It is also a stepping stone for new investigations and studies that goes beyond the facts about the composition and biochemistry of the connective tissue and extracellular matrix, as the authors connect individual components to specific aspects of various soft tissue disorders and to the actual or potential treatment of them"--
650 0 _aConnective tissues
650 1 2 _aConnective Tissue
650 1 2 _aConnective Tissue Diseases
650 1 2 _aConnective Tissue Disease
700 1 _aHalper, Jaroslava,
856 4 2 _uhttp://www.loc.gov/catdir/enhancements/fy1405/2014930168-d.html
856 4 1 _uhttp://www.loc.gov/catdir/enhancements/fy1405/2014930168-t.html
942 _cBK
999 _c1994
_d1994